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442《》0(2126CADASIL,22222【】:CADASIL。:174,5CT、MRI。:MIU,,,。:nU。:LnageRndingofCDoueKfei,uJiuZYaonet,al.1hetEdiiotralstaffofMMI71(X82lmaeCenter,iX,anGaanoHspi【Abstct]leS:oT,uthetimage6idngsnofcADASIL.MateadnMeht:ourF。ae8,ofcILi。。enly~seentd.iFveye。andMmfeatu℃5ofhetindexcase~。btain.Resis:Multivlelac~1fax℃itosnandle~osjowe,dinilleceerbiwltetmaettradnabsalgallia,espeicyhtexetemcapsadnaniterorpaZ’tofhteten1arllo,hcPorssedhthetage.nAaotrofhetbrainwasshowed.Concon:tImayidosedaCADASILifweeollinehetMIUifindngsiwhticlincfeat~1(1』yistItoyr·Keywo:CDAASILMaticersonanceimangc~infeiotnuconenonllvll(Ceerbalrauostomadominantar’tenopathyiwhtsubcortieinfacrstandleueoencephalopahty,CADSAIL)19pnothc3,〔`’],〔681、〔9l0jI“〕。、,4,,。1,49,。7,,,,23,、。1,,,,、,,、,。30,,,、,。。,,、。、,、,,,。,。,(1)。\\lL1CDAASIL():,,,100IHg,,。,27,9。,。,。、。。。V,。。(+),,。:、、、、、、、“o’,、、C、、DNA(71《】8)2MM1BIMONTHLYV6115No.6DecZ《X245、、、、HW、USR。:5CTMRI。Cr。MIU(5)lTiw,iw;(7)、Tl,WI;(3)、、lTwl,(2),-FIIR(3、4)。,、(4)。2、。3、4rrzw,huR、、、、,,、。22.1DASIL,45,。19938,19935CADSAIL,。2X()5400s[]。e[]s[]。〔`2〕、〔`3]。Nothc3。70%80%Nothc334。,,,(『anularohsahoniilcanIetir,GoM)。.s[’4]Nocth3GOM。;,,、、GOM。2.2,sj[,:(l),(rnA),85%。(2),60%,2/365。(3),,25,30%。(4),30%。10%,。,70,50、,,343,23。.23MlllCT,MRI、、、、MRS。2.3.1,、、、。7·“】。、。246《》20(1262.3.2、、,,、、、、,l[],35,30-40,50%,60,66%s[J。,,,,,。89%〔`,8、`。2.3.3MRI[5〕。2.3.42~,。、、、,2~10~,90%2~5~,82%’0]。2.3.5,ePet[’]76,,。.23.6(Dn)(facriotanlanisoyP)、,DTI,、,FA,vI[。2.3.7MRSNAA/Cr、NACh。、Cha/Cr,/Cr[3]。2.4CADAsIL,、。〔101。:(1),,;(2),,1;(3)MIR,;(4)GOM(45%,100%);(5)Nocth,4MIR100%。,MIR。1、2、3,DSAIL。31iShgnalS,chP,Mus.lesPiatalidbiutonofMRilllagnab~alltiesinceerbralautosomald~martaphyiwht51℃iortcalilestan〔1leukoeneePhalopathyIclhetireral-iotnsihpotageaJI〔】iclincfeat~A」NR.25;26(10):812489.2VandenBoolllR,lesckobosetinSA,vandenEnihsHuys-mans,etal.Ceerbralautosomaldonantartieropahtyiwht℃i6calillfarCtsandletoerleedat:sIctlu{alI」iagngcllangesalldaliOPportienEgell。,NR,2(x;29(2):359362.3MaeirM,ColoneneseC,GeffeG,etal.AellenitealsftimstudyonleignalmelaboilteidstubtlitoninaCDAASILfaJll-.MagneRsonhna119,2(X;24(4):27.4etPeN,H01tmannsoPettrM,OPhakrC,etbRalnv01ulnecI、angesinCDAASIL:asieralstudyinpuersubcoealiselle】evaseularsease.Neto,2(x;66(10):15171522.5PandeyT,AbubackerS.eCerbalralltosomaldomjIlnartena-iwhtsortalir`ctsleloellchenopat:aniamiggn。ofmultinleselerosis.Aerportofwotcases.MdeirPcnRaet,2X(;15(5):391395.6,,。5CADASIL。,2X()5,22(2):13513707,,。2CADASIL20。,2X()5,21(4):358~36()o8,,。CADASIL(l)。,2X()5,22(4):341309,。CADA51L。。22,2(1):6()61。10,,。CADASIL。,2,12(5):387390。11WIG,JIX,BalH,etal.StorkeersehinCihan.NeuoreRs.2X(;28(1):1116.12eRinGustvasenW,eRihnoltFP,cS】UosserA.ikSnbisyifnd-ignsan〔1ersultsofneuorpsyelloloigeetistgninhetifsrtcoinf~deasesofCADAILinNowr.EurJNell,2(;13(4):359362.13kielsaM,」hrasM,stikostasDD,CADASILasllorter-viewofhetliteartuerandadeseirptionOfhettinlyfl℃111Ceeree.FunctNen』01,2X(;21(2):7782.14cSllroderMJ,ZcuhnerS,iDcllglsM,et.ePirphealrnevredskeletalmusdeivllvolementinCADASIL.AetaNeuoraPhtol(eBlr),2X()5;110(6):587599.